TGA DORV TOF CCTGA

Core entities

  • Transposition of the Great Arteries (TGA)
  • Double Outlet Right Ventricle (DORV)
  • Tetralogy of Fallot (TOF)
  • Congenitally Corrected Transposition of the Great Arteries
Feature Tetralogy of Fallot Double Outlet Right Ventricle Transposition of the Great Arteries
Great arteries Crossing Crossing or abnormal Parallel
LV direct outlet Yes (partly) No Yes (to PA)
Aortic override 30–50% typical >50% (often >70%) None
VSD Large malalignment Always present Variable
Pulmonary artery Small Variable Normal
3-vessel view Small PA Variable Aorta anterior
LVOT continuity Present Absent Present
RVOT obstruction Typical Variable None
Feature TGA DORV TOF CCTGA
Great arteries Parallel Both from RV Crossing Parallel
LV connection To PA Often to VSD To overriding aorta To pulmonary artery
RV connection To Aorta To both vessels To overriding aorta To aorta
VSD Required for survival Always present Always present Variable
AV connections Normal Normal Normal Discordant

A. Transposition of the Great Arteries (TGA)

Parallel great arteries

Outflow tract:

  • Aorta arises from right ventricle
  • Pulmonary artery arises from left ventricle
  • No normal crossing

B. Double Outlet Right Ventricle (DORV)

Both great arteries arise predominantly from RV

VSD is mandatory.

LV has no direct outlet.

Instead: LV empties via VSD

Great arteries:

  • crossing present
  • abnormal alignment

C. Tetralogy of Fallot (TOF)

Classic tetrad:

  • VSD
  • Overriding aorta
  • RV hypertrophy
  • Pulmonary stenosis

Overriding aorta - Aorta sits: over VSD

Receiving blood from both ventricles.

Pulmonary artery: small

3-vessel view: Small pulmonary artery

D. Congenitally Corrected TGA (CCTGA)

Double discordance

  • AV discordance
  • VA discordance

Result: Circulation becomes "physiologically corrected."

Ventricular inversion

Right ventricle appears: on the left side

With:

  • moderator band
  • coarse trabeculation

Ventricular inversion

Great arteries:

Usually: parallel; Like TGA.

But: AV connections abnormal.