Azygous Vein and ARSA on Fetal Ultrasound

Azygous Vein and ARSA

Dilated azygos vein vs ARSA: core differences
• Azygos vein: venous structure, posterior, drains into the SVC.
• ARSA (aberrant right subclavian artery): arterial branch from the descending aorta, courses posterior to the trachea and esophagus.

Azygos → SVC (venous), ARSA → descending aorta (arterial).

Plane and position
Three-vessel–trachea (3VT) view
• ARSA
o Seen posterior to the trachea
o Usually oblique or horizontal
o Originates from the descending aorta

• Dilated azygos vein
o Seen posterior and to the right of the trachea
o More vertical or gently curving
o Joins the SVC superiorly

Doppler behavior

  Feature   Azygos vein   ARSA
  Doppler pattern   Low-velocity, phasic venous flow   High-velocity arterial flow
  Pulsatility   Respiratory variation   Cardiac pulsatility
  Color aliasing   Minimal   Common
  Direction   Toward SVC   Away from descending aorta

Connectivity tracing
• Trace inferiorly
o ARSA connects to descending aorta
o Azygos continues as a venous channel alongside the spine
• Trace superiorly
o Azygos drains into SVC
o ARSA goes to the right arm

ARSA
• Often isolated
• Soft marker for trisomy 21
• No venous enlargement elsewhere

Dilated azygos vein
• Often seen with:
o Interrupted IVC with azygos continuation
o Absent or hypoplastic ductus venosus
o Elevated central venous pressure
• SVC may appear prominent

When azygos vein is truly dilated
True azygos dilatation usually implies rerouted venous return
• Interrupted IVC with azygos continuation
• Absent ductus venosus
• Significant cardiac inflow obstruction

In these cases:
• Azygos vein is consistently large
• Seen in multiple planes
• Accompanied by systemic venous anomalies

If:
• Normal IVC
• Normal ductus venosus
• Normal venous Dopplers
and only a prominent vessel posterior to the trachea,
→ think physiologically prominent azygos,

The azygos vein is frequently visible
Especially in:
• Second and third trimester
• Thin maternal habitus
• Good venous color sensitivity
• When the left brachiocephalic vein is well seen

Left atrial isomerism (LAI), the azygos vein becomes the main venous pathway, not just a small accessory vein.

  Normal fetus   Left atrial heterotaxy
  IVC present   IVC interrupted
  Azygos is small or moderate   Azygos is large and dominant
  Venous return via IVC → RA   Venous return via azygos → SVC
  Often seen incidentally   Seen inevitably and prominently

Red flags
• IVC not seen below the liver
• “Double vessel” sign next to the descending aorta in abdominal view
• Large, straight, continuously visible azygos vein
• Abnormal hepatic venous drainage
• Cardiac clues:
o AVSD
o Bradyarrhythmia / heart block
o Abnormal pulmonary venous connections
• Visceral clues:
o Midline liver
o Stomach malposition
o Polysplenia

Azygos appearance
• Small to moderate calibre
• Curved, tapering • Intermittently conspicuous
• Best seen near SVC junction

→ NORMAL AZYGOS
vs • Large, straight, dominant vessel
• Seen in multiple planes continuously
• Runs parallel to descending aorta
• Comparable in size to SVC

→ PATHOLOGICAL AZYGOS
If ANY of the following are present, escalate:
• Midline liver
• Abnormal stomach position
• Polysplenia
• AVSD
• Bradycardia / heart block
• Abnormal pulmonary venous return
→ Think heterotaxy / left atrial isomerism